Medicine:Raymond-Céstan syndrome

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Raymond-Céstan syndrome
Other namesupper dorsal pontine syndrome,
Circle of Willis en.svg
Basillar artery runs down the middle(in above image) and blockage is cause of this condition

Raymond-Céstan syndrome is caused by blockage of the long circumferential branches of the basilar artery.[1] It was described by Fulgence Raymond and Étienne Jacques Marie Raymond Céstan.[2] Along with other related syndromes such as Millard-Gubler syndrome, Foville's syndrome, and Weber's syndrome, the description was instrumental in establishing important principles in brain-stem localization.[3]

Presentation

  • Ipsilateral ataxia and coarse intention tremor (damage to superior and middle cerebellar peduncle)
  • Ipsilateral paralysis of muscles of mastication and sensory loss in face (damage to sensory and motor nuclei and tracts of CN V)
  • Contralateral loss of sensory modalities in the body (damage to spinothalamic tract and medial lemniscus)
  • Contralateral hemiparesis of face and body (damage to corticospinal tract) may occur with ventral extension of lesion
  • Horizontal gaze palsy may occur (as in lower dorsal pontine syndrome)

Diagnosis

Treatment

References

  1. http://www.clineu-journal.com/article/S0303-8467(07)00181-3/abstract
  2. "Céstan-Chenais syndrome". http://www.whonamedit.com/synd.cfm/618.html. 
  3. Silverman, IE; Liu, GT; Volpe, NJ; Galetta, SL (June 1995). The crossed paralyses. The original brain-stem syndromes of Millard-Gubler, Foville, Weber, and Raymond-Cestan. Archives of Neurology. 52. pp. 635–8. doi:10.1001/archneur.1995.00540300117021. PMID 7763214. 

Further reading

  • Kim, JS; Lee, JH; Im, JH; Lee, MC (Jun 1995). "Syndromes of pontine base infarction. A clinical-radiological correlation study.". Stroke: A Journal of Cerebral Circulation 26 (6): 950–5. doi:10.1161/01.STR.26.6.950. PMID 7762044. 
  • Krasnianski, M; Neudecker, S; Zierz, S (Aug 2004). "[Classical crossed pontine syndromes]." (in German). Fortschritte der Neurologie · Psychiatrie 72 (8): 460–8. doi:10.1055/s-2004-818392. PMID 15305240.