Medicine:Ross' syndrome
| Ross' syndrome |
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Ross' syndrome consists of Adie's syndrome (myotonic pupils and absent deep tendon reflexes) plus segmental anhidrosis (typically associated with compensatory hyperhidrosis).[1]
It was characterized in 1958[2][3] by A.T. Ross.[4]
By 1992, eighteen cases had been documented.[5]
Signs and Symptoms
Initial manifestations often include an abnormal segmental sweating response (described as hyperhidrosis or anhidrosis in some patients) and a tonic pupil. Other commonly reported symptoms included fatigue, chronic cough, and increased urinary frequency.[6]
Prognosis
Ross syndrome is a non life-threatening benign condition but delay in diagnosis can result in slow progression of autonomic symptoms. [7]
Epidemiology
Ross Syndrome is a progressive autonomic dysfunction that can occur in any age, ethnicity, or gender. The average age of diagnosis for Ross syndrome is 36 years and affects more females than males.[7]
See also
- Hypohidrosis
- List of cutaneous conditions
References
- ↑ Dermatology: 2-Volume Set (2nd ed.). St. Louis: Mosby. 2007. pp. 539. ISBN 978-1-4160-2999-1.
- ↑ Otto Braun-Falco (2000). Dermatology. Springer. pp. 1093–. ISBN 978-3-540-59452-9. https://books.google.com/books?id=HkOty7O_KlkC&pg=PA1093. Retrieved 20 November 2010.
- ↑ "Ross syndrome: Unilateral hyperhidrosis, Adie's tonic pupils and diffuse areflexia". J Dtsch Dermatol Ges 8 (12): 1004–1006. April 2010. doi:10.1111/j.1610-0387.2010.07400.x. PMID 20408939.
- ↑ Ross AT (November 1958). "Progressive selective sudomotor denervation; a case with coexisting Adie's syndrome". Neurology 8 (11): 809–17. doi:10.1212/wnl.8.11.809. PMID 13590391.
- ↑ "Tonic pupil, areflexia, and segmental anhidrosis: two additional cases of Ross syndrome and review of the literature". J. Neurol. 239 (4): 231–4. April 1992. doi:10.1007/BF00839146. PMID 1597691.
- ↑ Lamotte, Guillaume; Sandroni, Paola; Cutsforth-Gregory, Jeremy K.; Berini, Sarah E.; Benarroch, Eduardo E.; Shouman, Kamal; Mauermann, Michelle L.; Anderson, Jennifer et al. (2021-10-01). "Clinical presentation and autonomic profile in Ross syndrome" (in en). Journal of Neurology 268 (10): 3852–3860. doi:10.1007/s00415-021-10531-8. ISSN 1432-1459. PMID 33813643. PMC 9639164. https://doi.org/10.1007/s00415-021-10531-8.
- ↑ 7.0 7.1 "Ross syndrome | DermNet NZ" (in en). https://dermnetnz.org/topics/ross-syndrome.
External links
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